Biochemistry › Protein Catabolism Intermediates
Phenylketonuria is a genetic disorder resulting in a lack of phenylalanine hydroxylase activity. During the first step of phenylalanine metabolism, phenylalanine is hydroxylated into what amino acid?
Tyrosine
Tryptophan
Serine
Threonine
Alanine
The first step in phenylalanine metabolism is conversion of phenylalanine to tyrosine. Tyrsoine is simply a hydroxylated version of phenylalanine.