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Example Question #10 : Protein Catabolism
Phenylketonuria is a genetic disorder resulting in a lack of phenylalanine hydroxylase activity. During the first step of phenylalanine metabolism, phenylalanine is hydroxylated into what amino acid?
The first step in phenylalanine metabolism is conversion of phenylalanine to tyrosine. Tyrsoine is simply a hydroxylated version of phenylalanine.